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It is generally associated with administration of gadolinium-based magnetic resonance imaging contrast agents (GBCA) in patients with kidney disease. [Orphanet:137617]","label":"nephrogenic systemic fibrosis","mondo":"MONDO:0015294","parents":["MONDO:0005093"],"synonym":{"exact":["nephrogenic fibrosing dermopathy"],"related":["NFD","NSF"]},"xrefs":{"gard":["0009725"],"icd11":["foundation:1537082562"],"icd9":["588.89"],"meddra":["10067467"],"medgen":["854737"],"mesh":["D054989"],"ncit":["C84920"],"nord":["1498"],"orphanet":["137617"],"sctid":["424114000"],"umls":["C3888044"]}},"original_id":["UMLS:C1619692","UMLS:C3888044"],"umls":[{"_license":"https://www.nlm.nih.gov/research/umls/knowledge_sources/metathesaurus/release/license_agreement.html","mesh":{"non-preferred":"D054989","preferred":"D054989"},"nci":{"preferred":"C84920"},"snomed":{"non-preferred":"424114000","preferred":"424114000"},"umls":"C1619692"},{"_license":"https://www.nlm.nih.gov/research/umls/knowledge_sources/metathesaurus/release/license_agreement.html","nci":{"non-preferred":"C115158","preferred":"C115158"},"snomed":{"non-preferred":"424114000","preferred":"424114000"},"umls":"C3888044"}]}