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syndrome (CCS) is a rare gastrointestinal (GI) polyposis syndrome characterized by the association of non-hereditary GI polyposis with the cutaneous triad of alopecia, nail changes and hyperpigmentation. [Orphanet:2930]","excluded_subClassOf":{"mondo":["MONDO:0006224"]},"label":"Cronkhite-Canada syndrome","mondo":"MONDO:0008283","parents":["MONDO:0004335","MONDO:0015185","MONDO:0019287"],"synonym":{"exact":["Cronkhite-Canada syndrome","gastric Cronkhite Canada polyposis","gastrointestinal polyposis-ectodermal changes syndrome","gastrointestinal polyposis-skin pigmentation-alopecia-fingernail changes syndrome"],"related":["Cronkhite-Canada disease","polyposis skin pigmentation alopecia fingernail changes"]},"xrefs":{"doid":["DOID:6225"],"gard":["0004427"],"icd11":["foundation:79007466"],"meddra":["10062907"],"medgen":["129128"],"mesh":["D044483"],"nando":["1200901"],"ncit":["C7035"],"nord":["1017"],"omim":["175500"],"orphanet":["2930"],"sctid":["76304001"],"umls":["C0282207"]}},"umls":{"_license":"https://www.nlm.nih.gov/research/umls/knowledge_sources/metathesaurus/release/license_agreement.html","mesh":{"non-preferred":"D000098858","preferred":"D000098858"},"snomed":{"non-preferred":"76304001","preferred":"76304001"},"umls":"C0282207"}}