{"_id":"MONDO:0005615","_version":1,"ctd":{"chemical_related_to_disease":[{"chemical_name":"Bortezomib","direct_evidence":"therapeutic","mesh_chemical_id":"D000069286","pubmed":["19259673","22262760"],"source":"CTD"},{"cas_registry_number":"1921-70-6","chemical_name":"pristane","direct_evidence":"marker/mechanism","mesh_chemical_id":"C009042","pubmed":"15087411","source":"CTD"},{"chemical_name":"ricolinostat","direct_evidence":"therapeutic","mesh_chemical_id":"C572255","pubmed":"22262760","source":"CTD"},{"chemical_name":"Rosiglitazone","direct_evidence":"therapeutic","mesh_chemical_id":"D000077154","pubmed":"19731824","source":"CTD"},{"cas_registry_number":"7782-49-2","chemical_name":"Selenium","direct_evidence":"marker/mechanism","mesh_chemical_id":"D012643","pubmed":"15087411","source":"CTD"},{"cas_registry_number":"302-79-4","chemical_name":"Tretinoin","direct_evidence":"therapeutic","mesh_chemical_id":"D014212","pubmed":"19731824","source":"CTD"}],"mesh":"D010954"},"disease_ontology":{"_license":"https://github.com/DiseaseOntology/HumanDiseaseOntology/blob/master/DO_LICENSE.txt","ancestors":["DOID:0060083","DOID:707","DOID:0060073","DOID:14566","DOID:4","DOID:162","DOID:6536","DOID:0060060","DOID:75","DOID:2914","DOID:2531","DOID:0060058","DOID:74","DOID:7","DOID:706","DOID:0050686"],"children":["DOID:3720","DOID:3722","DOID:3723"],"def":"","descendants":["DOID:3720","DOID:3722","DOID:3723"],"doid":"DOID:3721","name":"plasmacytoma","parents":["DOID:6536"],"synonyms":{"exact":["Myeloma - solitary","Myeloma, solitary","Solitary myeloma","Solitary plasmacytoma"]},"xrefs":{"icd10":"C90.3","icdo":"9731/3","mesh":"D010954","ncit":"C9349","snomedct_us_2025_09_01":"302852008","umls_cui":"C0032131"}},"mondo":{"ancestors":["MONDO:0004959","MONDO:0004949","MONDO:0000001","MONDO:0045024","MONDO:0005570","MONDO:0002334","MONDO:0005157","MONDO:0004805","MONDO:0044881","MONDO:7770008","MONDO:0005062","MONDO:0005070","MONDO:7770006","MONDO:0005046","MONDO:0023370","MONDO:0700096","MONDO:0004095","MONDO:0015757"],"children":["MONDO:0002754","MONDO:0002755","MONDO:0002756","MONDO:0015042","MONDO:0015043"],"definition":"Plasmacytoma is a localized mass of neoplastic monoclonal plasma cells that represents approximately 5% of all plasma cell neoplasms. There are two separate entities: primary plasmacytoma of the bone and extramedullary plasmacytoma of the soft tissues. Of the extramedullary plasmacytomas, 80% occur in the head and neck, usually in the upper respiratory tract. The median age at diagnosis is 50 years and the male to female ratio is 3:1. Long-term survival is possible following local radiotherapy, particularly for soft tissue presentations. [Orphanet:86855]","descendants":["MONDO:0002754","MONDO:0002756","MONDO:0002755","MONDO:0015042","MONDO:0015043"],"label":"plasmacytoma","mondo":"MONDO:0005615","parents":["MONDO:0004959"],"synonym":{"exact":["plasmacytoma"],"related":["anaplastic plasmacytoma","anaplastic skeletal plasmacytoma (type)","anaplastic solitary extramedullary plasmacytoma of the cecum (type)","extramedullary anaplastic plasmacytoma (type)"]},"xrefs":{"doid":["DOID:3721"],"efo":["EFO:0006738"],"gard":["0013446"],"icd11":["foundation:1811140613"],"icd9":["238.6"],"icdo":["9731/3"],"meddra":["10035484"],"medgen":["18506"],"mesh":["D010954"],"ncit":["C9349"],"orphanet":["86855"],"sctid":["415112005"],"umls":["C0032131"]}},"umls":{"_license":"https://www.nlm.nih.gov/research/umls/knowledge_sources/metathesaurus/release/license_agreement.html","icd10am":{"preferred":"M9731/3"},"icd10cm":{"non-preferred":["C90.30","C90.3"],"preferred":"C90.3"},"mesh":{"non-preferred":"D010954","preferred":"D010954"},"nci":{"non-preferred":"C6932","preferred":"C9349"},"snomed":{"non-preferred":["188720009","189507001","302852008","1187107005","188719003","190019006","109987008","274907000","190017008","269652000","154644004","308122007","190016004","415112005","10639003"],"preferred":["188720009","302852008","189507001","1187107005","188719003","308122007","415112005","10639003"]},"umls":"C0032131"}}